Micronodular PEComa of the appendix: a case report - Report - MDSpire

Micronodular PEComa of the appendix: a case report

  • By

  • Li-Jing Jiang

  • Chao-Qun Wang

  • Zheng-Guo Xu

  • May 22, 2026

  • 0 min

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Clinical Report: Micronodular Perivascular Epithelioid Cell Tumor of the Appendix

Overview

{'add': "Specify the duration of follow-up and detail the nature of 'significant improvement'."}

Background

{'add': 'Discuss the clinical implications of misdiagnosis and management strategies.'}

Data Highlights

{'edit': 'Revise to indicate the absence of numerical data but mention qualitative findings.'}

Key Findings

{'edit': 'Ensure TFE3 positivity is included in the immunohistochemical analysis.'}

Clinical Implications

{'edit': 'Include management strategies post-diagnosis and the importance of follow-up.'}

Conclusion

{'edit': 'Highlight the necessity for further research and case accumulation.'}

Related Resources & Content

  1. Tran T.A.N., Fanaian N., 2020 -- Local PEComatosis of the Appendix: New Insights Into the Histogenesis of Nodular Granular Muscle Degeneration and Granular Cells/Granular Cell Lesions of the Appendix
  2. NCCN Guidelines® Insights: Soft Tissue Sarcoma, Version 1.2025 - PubMed
  3. Frontiers in Oncology — Localized peritoneal epithelioid clear cell subtype mesothelioma: a case report and literature review
  4. Journal of Gastrointestinal Surgery — Appendiceal Carcinoid Tumors: A Study of 1,485 Consecutive Emergency Appendectomies
  5. Pediatric Inflammatory Myofibroblastic Tumors of the Colon: Clinical Features, Treatment Approaches, and Outcomes—A Case Study with a Comprehensive Literature Review
  6. Investigating Active Surveillance Strategies for Papillary Microcarcinoma of the Thyroid in Clinical Trials
  7. Local PEComatosis of the Appendix: New Insights Into the Histogenesis of Nodular Granular Muscle Degeneration and Granular Cells/Granular Cell Lesions of the Appendix - Tien Anh N. Tran, Na’im Fanaian, 2020
  8. NCCN Guidelines® Insights: Soft Tissue Sarcoma, Version 1.2025 - PubMed
  9. Nab-sirolimus in Advanced Malignant Perivascular Epithelioid Cell Tumors AMPECT Trial Final Analysis - The ASCO Post

Original Source(s)

Micronodular PEComa of the appendix: a case report

  • by Li-Jing Jiang, Chao-Qun Wang, Zheng-Guo Xu

  • May 22, 2026

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