Correction: Sjögren’s syndrome–associated fulminant myocarditis presenting as cardiogenic shock requiring VA-ECMO: a case report - Report - MDSpire
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Amendment: Fulminant Myocarditis Linked to Sjögren’s Syndrome Manifesting as Cardiogenic Shock Necessitating VA-ECMO: A Case Study

  • By

  • Thanh Hoa Tran

  • Quoc Thang Le

  • Thao My Doan Ai

  • Sinh Hien Nguyen

  • September 25, 2026

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Clinical Report: Fulminant Myocarditis Linked to Sjögren’s Syndrome

Background

Fulminant myocarditis is a rare but severe inflammatory condition of the myocardium that can lead to significant morbidity and mortality. It often presents as cardiogenic shock, necessitating advanced therapeutic interventions such as temporary mechanical circulatory support.

Data Highlights

No numerical data or trial data is provided in the source material.

Key Findings

  • Fulminant myocarditis can manifest as cardiogenic shock, requiring advanced support.
  • Temporary mechanical circulatory support (MCS) is increasingly utilized in managing cardiogenic shock.
  • Systemic immune-mediated diseases are recognized as potential noninfectious causes of myocarditis.
  • VA-ECMO is a critical intervention for patients with refractory cardiogenic shock.

Clinical Implications

Healthcare professionals should be aware of the potential for fulminant myocarditis in patients with autoimmune conditions such as Sjögren’s syndrome.

Conclusion

The case highlights the importance of recognizing fulminant myocarditis in the context of autoimmune diseases.

Related Resources & Content

  1. Tran TH, Nguyen SH, BMC Cardiovascular Disorders, 2025 -- Fulminant Myocarditis Linked to Sjögren’s Syndrome
  2. Clinical Research in Cardiology — Impact of Combined VAV-ECMO, Impella CP, and Impella RP on Hemodynamics
  3. Critical Care — Assessment of Left Ventricular Decompression During VA-ECMO in Patients with Refractory Cardiogenic Shock: A Multicenter Target Trial Emulation Study
  4. Intensive Care Medicine — Temporary mechanical circulatory support in fulminant myocarditis: can global collaborations bridge the gap?
  5. Frontiers in Cardiovascular Medicine — Case Report: When inotropy backfires—dobutamine-associated eosinophilic myocarditis
  6. 2025 ESC Guidelines for the management of myocarditis and pericarditis
  7. ELSO Interim Guidelines for Venoarterial Extracorporeal Membrane Oxygenation in Adult Cardiac Patients
  8. Sjögren's syndrome-associated fulminant myocarditis presenting as cardiogenic shock requiring VA-ECMO: a case report - PubMed

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