Case Report: Unrepaired Tetralogy of Fallot in a 50-year-Old woman with 13 pregnancies: multimodal cardiovascular imaging, surgical repair, and longitudinal remodeling - Scorecard - MDSpire
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Case Report: Unrepaired Tetralogy of Fallot in a 50-year-Old woman with 13 pregnancies: multimodal cardiovascular imaging, surgical repair, and longitudinal remodeling
Clinical Scorecard: Case Study: A 50-Year-Old Woman with Uncorrected Tetralogy of Fallot and 13 Pregnancies: Comprehensive Cardiovascular Imaging, Surgical Intervention, and Long-Term Cardiac Remodeling
At a Glance
Category
Detail
Condition
Tetralogy of Fallot
Key Mechanisms
Characterized by ventricular septal defect, right ventricular outflow tract obstruction, overriding aorta, and right ventricular hypertrophy.
Target Population
Adults with uncorrected Tetralogy of Fallot, particularly women with multiple pregnancies.
Care Setting
Cardiology and congenital heart disease management
Key Highlights
Only 3%-5% of patients with uncorrected TOF survive to age 40.
Multimodal cardiovascular imaging is crucial for diagnosis and surgical planning.
Successful corrective surgery led to normalization of oxygen saturation.
Postoperative echocardiography showed significant reduction in RV/RA dimensions.
Awareness of congenital heart disease in adults is essential for timely diagnosis.
Guideline-Based Recommendations
Diagnosis
Use multimodal cardiovascular imaging for late diagnoses of congenital heart disease.
Management
Consider surgical intervention for adults with uncorrected TOF presenting with symptoms.
Monitoring & Follow-up
Serial echocardiography to assess postoperative cardiac remodeling and residual obstruction.
Risks
Hypoxic spells, cerebrovascular events, and brain abscesses are common causes of death in untreated TOF.
Patient & Prescribing Data
Adult women with a history of multiple pregnancies and unrecognized congenital heart disease.
Surgical intervention can be safe and effective even in late presentations.
Clinical Best Practices
Routine evaluation of oxygen saturation in adults, especially those with unexplained cyanosis.
Strengthened awareness among healthcare providers regarding congenital heart disease in adults.
by Moath Hattab, Yahya Ismail, Ahmed Darsalim, Nour Deek, Mohammad Abed, Adham Abderrazeq, Abelhalim Abuhaltam, Mohammed SalahAldin, Mohammed Abutaqa, Nizar Hijjeh
