Primary orbital solitary fibrous tumor with an 18-year course of five recurrences and extensive sinonasal metastasis following eyeball enucleation: a case report - Scorecard - MDSpire

Primary orbital solitary fibrous tumor with an 18-year course of five recurrences and extensive sinonasal metastasis following eyeball enucleation: a case report

  • By

  • Jiayin Cai

  • Yijia Zhang

  • Jiabei Xiong

  • Xiaoxiao Luo

  • Yiyao Wang

  • Yongping Hu

  • Xiaolin Cao

  • Jianguang Zhong

  • Jian Li

  • May 22, 2026

  • 0 min

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Clinical Scorecard: Long-Term Case Study of a Primary Orbital Solitary Fibrous Tumor with Multiple Recurrences and Extensive Sinonasal Metastasis After Eyeball Enucleation

At a Glance

CategoryDetail
Condition
Key Mechanisms
Target PopulationAdults aged 50 and above with orbital solitary fibrous tumors.
Care Setting

Key Highlights

  • Histopathological analysis confirmed the diagnosis with nuclear STAT6 positivity.

Guideline-Based Recommendations

Diagnosis

    Management

      Monitoring & Follow-up

      • Lifelong clinical and systemic imaging surveillance is advised, including MRI and CT scans.

      Risks

        Patient & Prescribing Data

        Multiple surgical interventions, including resection and orbital exenteration, were required due to recurrences.

        Clinical Best Practices

        • Early intervention with complete surgical excision.
        • Integration of adjuvant therapies for aggressive cases.
        • Regular follow-up imaging to monitor for recurrence.
        • Collaboration with a multidisciplinary team for comprehensive management.

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        Original Source(s)

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