Objective:

To present a case of neurosarcoidosis in a patient with acute zonal occult outer retinopathy, emphasizing the diagnostic challenges and treatment outcomes in the context of this rare condition.

Key Findings:

• Neurosarcoidosis can present with ocular symptoms, complicating diagnosis and requiring careful consideration.
• Elevated angiotensin-converting enzyme levels and granulomatous inflammation confirmed sarcoidosis, underscoring the need for thorough diagnostic workup.
• Prompt treatment led to resolution of neurological and ophthalmic symptoms, demonstrating the effectiveness of early intervention.

Interpretation:

This case underscores the importance of considering neurosarcoidosis in patients with unexplained neurological symptoms, particularly those with ocular involvement, given its rarity.

Limitations:

• The rarity of neurosarcoidosis may limit generalizability of findings and awareness among clinicians.
• Diagnosis often relies on exclusion of other conditions, which can delay treatment and complicate patient management.

Conclusion:

Neurosarcoidosis should be considered in patients with neurological symptoms and ocular involvement, as timely diagnosis and treatment can lead to significant recovery, emphasizing the need for interdisciplinary collaboration.