Follicular dendritic cell sarcoma associated with IgG4-related disease: a case report and literature review - Takeaways - MDSpire

Follicular dendritic cell sarcoma associated with IgG4-related disease: a case report and literature review

  • By

  • Yajuan Yao

  • Yunjing Bai

  • Guang Liu

  • Yu Du

  • Xiaoyu Long

  • Xiaohua Xu

  • Fan Wu

  • Xiaorong Jin

  • May 29, 2026

  • 0 min

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  • 1

    Follicular dendritic cell sarcoma (FDCS) is a rare malignant tumor that can affect lymph nodes and extranodal sites.

  • 2

    The inflammatory pseudotumor (IPT)-like variant of FDCS primarily involves the liver and spleen.

  • 3

    IgG4-related disease (IgG4-RD) is characterized by elevated serum IgG4 levels and multiorgan involvement.

  • 4

    This case presents a unique instance of FDCS associated with IgG4-RD, involving the liver, esophagus, and stomach.

  • 5

    The patient experienced improvement in gastrointestinal lesions after therapy, but the hepatic lesion progressed and was confirmed as FDCS.

Original Source(s)

Follicular dendritic cell sarcoma associated with IgG4-related disease: a case report and literature review

  • by Yajuan Yao, Yunjing Bai, Guang Liu, Yu Du, Xiaoyu Long, Xiaohua Xu, Fan Wu, Xiaorong Jin

  • May 29, 2026

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