Percutaneous Closure of Multiple Large Coronary Fistulae and Right Ventricular Outflow Tract Opening to Establish Biventricular Circulation in a Child with Pulmonary Atresia and Intact Ventricular Septum – A Case Report - Takeaways - MDSpire
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Catheter-Based Closure of Multiple Large Coronary Fistulae and Right Ventricular Outflow Tract Intervention to Achieve Biventricular Circulation in a Pediatric Patient with Pulmonary Atresia and Intact Ventricular Septum – A Case Study

  • By

  • Julia Danner

  • Peter Ewert

  • Katarzyna Gendera

  • July 9, 2026

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  • 1

    A 24-day-old male with pulmonary atresia and large RV-to-coronary fistulae underwent catheter-based interventions to achieve biventricular physiology.

  • 2

    Initial assessments revealed a hypoplastic tricuspid valve and severely narrowed right ventricular outflow tract, complicating treatment decisions.

  • 3

    Multiple coronary fistulae were successfully closed using Amplatzer devices, with careful monitoring of myocardial perfusion during procedures.

  • 4

    Despite interventions, the right ventricular pressure remained suprasystemic, necessitating further procedures including RVOT resection at 12 months.

  • 5

    At 22 months, the patient showed normal oxygen saturation and preserved biventricular function, continuing anticoagulation therapy postoperatively.

Original Source(s)

Percutaneous Closure of Multiple Large Coronary Fistulae and Right Ventricular Outflow Tract Opening to Establish Biventricular Circulation in a Child with Pulmonary Atresia and Intact Ventricular Septum – A Case Report

  • by Julia Danner, Peter Ewert, Katarzyna Gendera

  • July 9, 2026

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