A congenital portosystemic shunt in the neonatal period: case report and literature review - Takeaways - MDSpire

A congenital portosystemic shunt in the neonatal period: case report and literature review

  • By

  • Li Cheng

  • Shuwen Feng

  • Yin Shen

  • Xia Wang

  • Bingyan He

  • Dongchi Zhao

  • Pu Yang

  • July 15, 2026

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  • 1

    Congenital portosystemic shunt (CPSS) is a rare malformation of the portal venous system, with an incidence of approximately 1/50,000–1/30,000.

  • 2

    Neonates with CPSS may present with respiratory distress, diffuse ecchymosis, petechial hemorrhages, and progressive liver dysfunction.

  • 3

    Diagnosis of CPSS can be challenging due to vague clinical manifestations, often leading to misdiagnosis in the neonatal period.

  • 4

    Current treatments for CPSS include conservative management, endovascular embolization, surgical ligation, and liver transplantation.

  • 5

    Early detection and systematic assessment are crucial for improving outcomes in neonates with CPSS.

Original Source(s)

A congenital portosystemic shunt in the neonatal period: case report and literature review

  • by Li Cheng, Shuwen Feng, Yin Shen, Xia Wang, Bingyan He, Dongchi Zhao, Pu Yang

  • July 15, 2026

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