Nasal kaposiform hemangioendothelioma: a rare disease in a rare location—a review article with a case report - Takeaways - MDSpire

Nasal kaposiform hemangioendothelioma: a rare disease in a rare location—a review article with a case report

  • By

  • Feras Alkholaiwi

  • Ji Yun Choi

  • May 13, 2026

  • 0 min

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  • 1

    Kaposiform hemangioendothelioma is a rare vascular neoplasm primarily affecting infants, but can occur in adults, as seen in a 59-year-old female case.

  • 2

    The tumor typically presents as painful, enlarging lesions and is most commonly found in the retroperitoneum and skin, with rare occurrences in the nasal region.

  • 3

    The patient experienced nasal obstruction and epistaxis, with imaging revealing a mass in the right inferior turbinate, leading to endoscopic resection.

  • 4

    Histopathological evaluation confirmed the diagnosis, showing positivity for CD34 and CD31, and no recurrence was observed after 5 months of follow-up.

  • 5

    Kaposiform hemangioendothelioma is classified by the WHO as having intermediate malignant potential, with a propensity for local invasion and lymph node dissemination.

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