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1
Very Long Chain Acyl-CoA Dehydrogenase Deficiency (VLCADD) impairs mitochondrial oxidation of long-chain fatty acids, leading to significant metabolic risks.
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2
A multidisciplinary team approach was essential for the perioperative management of a 65-year-old female patient with VLCADD undergoing laparoscopic sleeve gastrectomy.
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3
Key management strategies included minimizing fasting, continuous glucose infusion, and careful selection of anesthetic agents to prevent metabolic crises.
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4
Postoperative complications included rhabdomyolysis, with creatine kinase levels rising significantly, necessitating aggressive fluid management and monitoring.
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5
At follow-up, the patient showed significant weight loss, improved diabetes control, and no further episodes of rhabdomyolysis, indicating successful management.
