Primary sclerosing epithelioid fibrosarcoma of the iliac fossa: a case report

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Sclerosing epithelioid fibrosarcoma (SEF) is a rare and aggressive fibroblastic malignancy, with primary iliac fossa involvement being exceptionally uncommon.
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A 53-year-old man presented with a painful mass in the right lower quadrant, diagnosed as SEF after imaging and histopathological examination.
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Imaging revealed a well-circumscribed lesion with heterogeneous low density on CT and mixed hyperintensity on MRI, aiding in diagnosis.
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Differential diagnoses included solitary fibrous tumor and low-grade fibromyxoid sarcoma, ruled out by characteristic imaging and histopathological features.
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Radical surgical resection is the primary treatment for SEF, with the case showing no evidence of recurrence or metastasis during 10 months of follow-up.

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