Intravenous leiomyomatosis manifesting as a cardiac mass: a case report - Takeaways - MDSpire

Intravenous leiomyomatosis manifesting as a cardiac mass: a case report

  • By

  • Haoxuan Deng

  • Qiyue Zhu

  • Wei Qiu

  • Yunyan Zhang

  • Junyi Hua

  • June 2, 2026

  • 0 min

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  • 1

    A 45-year-old woman with intravenous leiomyomatosis presented with chest tightness, initially diagnosed as a cardiac mass.

  • 2

    Multimodal imaging revealed IVL extending from pelvic veins through the inferior vena cava into the right atrium.

  • 3

    Histopathological examinations confirmed IVL with positive markers including α-SMA, desmin, CD10, ER, and PR.

  • 4

    The case highlights the rarity of IVL presenting as a cardiac mass and the importance of multidisciplinary diagnosis.

  • 5

    Short-term postoperative imaging data are available, but long-term follow-up is ongoing due to IVL's recurrence risk.

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