Case Report: A rare pediatric case of secretory carcinoma of the parotid gland with high-grade components misdiagnosed as pleomorphic adenoma

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Secretory carcinoma of the parotid gland is a rare malignant tumor in children, often misdiagnosed as pleomorphic adenoma due to similar clinical features.
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A 12-year-old boy presented with a left parotid mass, initially diagnosed via FNAC as pleomorphic adenoma, highlighting diagnostic challenges.
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Histopathological examination revealed high-grade secretory carcinoma with distinct features, including ETV6::NTRK3 gene fusion confirmed by FISH.
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The patient underwent successful superficial parotidectomy and functional neck dissection, with no need for adjuvant therapy postoperatively.
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At 29 months follow-up, the patient remained disease-free, underscoring the importance of accurate diagnosis and management of pediatric salivary gland tumors.

Frontiers In Oncology

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