Case Report: A “visceral vasculitis storm” in Systemic Lupus Erythematosus: simultaneous enteritis, ureteritis, and splenic infarction in a pediatric patient - Takeaways - MDSpire

Case Report: A “visceral vasculitis storm” in Systemic Lupus Erythematosus: simultaneous enteritis, ureteritis, and splenic infarction in a pediatric patient

  • By

  • Xia Wu

  • Yan Liu

  • Huan He

  • July 9, 2026

  • 0 min

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  • 1

    Systemic Lupus Erythematosus (SLE) can manifest as visceral vasculitis, including lupus enteritis and rare lupus ureteritis.

  • 2

    A 16-year-old girl presented with abdominal pain, fever, and transient dysuria, leading to a diagnosis of SLE with diffuse visceral vasculitis.

  • 3

    Contrast-enhanced CT revealed distinct ureteral wall enhancement, aiding in the diagnosis of primary lupus ureteritis.

  • 4

    The patient responded rapidly to methylprednisolone pulse therapy and IVIG, followed by maintenance therapy with Cyclophosphamide.

  • 5

    Recognizing the 'visceral vasculitis storm' is crucial for timely immunosuppressive therapy to prevent irreversible organ damage.

Original Source(s)

Case Report: A “visceral vasculitis storm” in Systemic Lupus Erythematosus: simultaneous enteritis, ureteritis, and splenic infarction in a pediatric patient

  • by Xia Wu, Yan Liu, Huan He

  • July 9, 2026

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