Emergency in pediatric rheumatology: a narrative review - Takeaways - MDSpire

Emergency in pediatric rheumatology: a narrative review

  • By

  • Francesca Casini

  • Luca Bernardo

  • Clelia Di Mari

  • Marta Brambilla

  • Lisa Gamalero

  • Martina Sandini

  • Sara Rotunno

  • Emanuele Bizzi

  • Angela Mauro

  • Teresa Giani

  • May 18, 2026

  • 0 min

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  • 1

    Emergencies in pediatric rheumatology are rare but require rapid diagnosis and treatment to minimize mortality and morbidity.

  • 2

    Misdiagnosis is common in pediatric rheumatology emergencies, necessitating prompt recognition and management.

  • 3

    The review categorizes emergencies by pathology, detailing epidemiology, clinical presentation, diagnosis, and therapy.

  • 4

    Catastrophic antiphospholipid syndrome (CAPS) is a severe, life-threatening condition characterized by rapid thrombosis and multiorgan failure.

  • 5

    Pediatric CAPS often presents with primary antiphospholipid syndrome and is frequently triggered by infections or disease flares.

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