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1
Polymorphous low-grade neuroepithelial tumor of the young (PLNTY) primarily presents as drug-resistant epilepsy, often diagnosed in adolescents.
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2
Imaging typically shows atypical features, such as hypointensity on T2-weighted MRI, complicating diagnosis and potentially leading to misinterpretation.
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3
Definitive diagnosis of PLNTY requires a combination of pathological morphology, immunohistochemistry, and molecular testing, including BRAF mutation analysis.
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4
Gross total resection of PLNTY significantly reduces or eliminates seizures, resulting in a favorable prognosis for patients.
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5
Fewer than 100 cases of PLNTY have been reported, highlighting the need for increased awareness and understanding of this rare tumor.
